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Stargardt's Disease
Stargardt's Disease is a form of macular degeneration that causes
gradual loss of central vision due to the degeneraton of the cone
receptor cells. Cones are concentrated in the macula (the area responsible
for detailed central vision) and aid in color perception and detailed
sight. This disease afftects both eyes but does not harm peripheral
vision. Over time, a hole forms in the central vision and colors
can no longer be perceived.
Stargardt's disease is genetically passed from generation to generation.
In order for subsequent generation to get Stargardt's disease, both
parents must carry the recessive gene and even then, the children
of the gene carriers only have a 25% chance of developing the disease.
Signs and Symptoms
gradual
loss of vision
gray or black
area in the center of vision
blurry vision
not correctable with glasses
can't adapt
to changes in light very well
Diagnosis
A dilated fundus exam is required. In children complaining of
poor vision, diagnosis may be difficult. Over time, it will become
more evident during examinations. For testing, electrodiagnostic
tests, color vision tests, visual field tests, and fluorescein angiograms
may be performed.
Treatment
Unfortunately there is no effective treatment for Stargardt's
disease. For leaking blood vessels, laser treatments may be performed
to help stabilize some vision.

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information for educational and communication purposes only and
it should not be construed as medical advice. Information published
on this website is not intended to replace, supplant, or augment
a consultation with an retina professional regarding the viewer's
own medical care. The Retina Eye Center disclaims any and all liability
for injury or other damages that could result from use of the information
obtained from this site.
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